1. Abstract
1.1. Introduction Castleman’s disease (CD), described in 1956, is characterized as a low-incidence lymphoproliferative disorder with varied clinical manifestations, from asymptomatic to severe disseminated forms. The diagnosis is confirmed by histopathology and immunohistochemistry and should be considered after more common lymphoid diseases have been ruled out. This paper aims to describe a case of CD as a retroperitoneal tumor.