1.1. Introduction: Aplasia cutis congenital (ACC) is a heteroge neous group of disorders that share a common feature of focal skin loss. In most cases, this is limited to the scalp, also involve other parts of the body. (ACC) is a heterogeneous group of disorders whose common characteristic is focal absence of skin. In the ma jority of instances this is limited to the scalp, although other areas of the body may also be involved. It is characterized by a lack of skin and adjacent tissues, and it can extend into underlying tis sues, such as muscle tissue and bone, that can be underdeveloped or even absent. ACC can be life-threatening in severe cases. Both conservative and surgical approaches carry risks, and the timing of surgery remains controversial.